Dentin Dysplasia Type I with Hypomature Amelogenesis Imperfecta in an 18-year-old Girl

Authors

  • Ehsan Azma Department of Oral Medicine, Guilan University of Medical Sciences, Dental School, Rasht, Iran
  • Seyed Javad Kia Department of Oral Medicine, Guilan University of Medical Sciences, Dental School, Rasht, Iran
  • Somayeh Nemati Department of Maxillofacial Radiology, Guilan University of Medical Sciences, Dental Faculty, Rasht, Iran
Abstract:

Introduction: Dentin dysplasia is a rare autosomal dominant inheriting disturbance of dentin formation characterized by normal enamel formation, but atypical dentin with abnormal pulpal morphology. There are two major patterns: type I and type II. Amelogenesis imperfecta is an autosomal dominant. X-link inherent disease that is classified by clinical manifestation into hypoplastic, hypomature, hypocalcified. The simultaneous occurrence of dentin dysplasia and amelogenesis imperfecta is quite rare. The purpose of this case report is to pre-sent a case of dentin dysplasia type I which is also associated with hypoplastic amelogenesis imperfecta in an 18 year old girl, without any syndromic signs.

Upgrade to premium to download articles

Sign up to access the full text

Already have an account?login

similar resources

dentin dysplasia type i with hypomature amelogenesis imperfecta in an 18-year-old girl

introduction: dentin dysplasia is a rare autosomal dominant inheriting disturbance of dentin formation characterized by normal enamel formation, but atypical dentin with abnormal pulpal morphology. there are two major patterns: type i and type ii. amelogenesis imperfecta is an autosomal dominant. x-link inherent disease that is classified by clinical manifestation into hypoplastic, hypomature, ...

full text

Association of Behçet’s Disease with Osteogenesis Imperfecta in A Ten-Year-Old Girl

Osteogenesis Imperfecta (OI) is a genetic disorder characterized by bones that break easily, often from little or no apparent cause. In this article, we present a patient suffering from OI, who had concomitant active Behçet’s Disease(BD)with repeated oro-genital ulcers, skin postular eruptions and severe recurrent bilateral uveitis. This patient, is, to our knowledge the first reported case in ...

full text

Gastric tricho-wool bezoar in an 18-year-old girl.

An 18-year-old girl with no psychiatric history presented with abdominal pain. Four months previously she had given birth to a healthy baby. On palpation, a painful abdominal mass was identified in the epigastric region, and gastrotomy was performed. A J-shaped hair-wool ball and two large pieces of sheep's wool were removed. No history of trichotillomania was reported.

full text

Restoring Aesthetics and Function in a Young Boy with Hypomature Amelogenesis Imperfecta: A Case Report

Amelogenesis imperfecta has been described as a complex group of inherited conditions that disturbs the developing enamel structure and exists independent of any related systemic disorder. It is a rare dental disease but represents a great restorative challenge for dentists. A 12-year-old boy presented with sensitive, discolored, and mutilated teeth and decreased vertical dimension of occlusion...

full text

CASE REPORT Dentin dysplasia type I

To cite: Singh A, Gupta S, Yuwanati MB, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2013009403 SUMMARY Dentin dysplasia type I is a rare hereditary disturbance of dentin formation characterised clinically by nearly normal appearing crowns and hypermobility of teeth that affects one in every 100 000 individuals and manifests in both primary and permanent...

full text

Dentin dysplasia type I--a case report.

A case report on dentin dysplasia type I, a congenital disease (autosomal dominant gene defect) affecting deciduous and permanent teeth, is depicted including representations of clinical and histological features, X-ray and CT-findings. Therapy includes extraction of all teeth, ectomization of cystic alteration, revision of paranasal sinus. Aesthetic and functional rehabilitation by means of in...

full text

My Resources

Save resource for easier access later

Save to my library Already added to my library

{@ msg_add @}


Journal title

volume 2  issue 3

pages  34- 39

publication date 2013-10

By following a journal you will be notified via email when a new issue of this journal is published.

Keywords

Hosted on Doprax cloud platform doprax.com

copyright © 2015-2023